megacystis microcolon intestinal hypoperistalsis syndrome: report of a rare case in newborn

نویسندگان

saeid tarlan department of pediatric surgery, school of medicine, qazvin university of medical sciences, qazvin, iran.

abolfazl mahyar department of pediatric, school of medicine, qazvin university of medical sciences, qazvin, iran.

victoria chegini department of pediatric, school of medicine, qazvin university of medical sciences, qazvin, iran.

venus chegini 3department of gynecology, school of medicine, tehran university of medical science, tehran, iran.

چکیده

megacystis microcolon intestinal hypoperistalsis syndrome (mmihs) is a rare and the most severe form of functional intestinal obstruction in the newborn. the characteristic features of this congenital and fatal disease are abdominal distension, absent or decreased bowel peristalsis. abdominal distension is a consequence of the distended, unobstructed urinary bladder with or without hydronephrosis. we present a case of female newborn with antenatal ultrasound revealing a large cystic mass in pelvic with urinary tract origin, abdominal distension, aperistalsis of the intestine and micro colon.

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عنوان ژورنال:
acta medica iranica

جلد ۵۳، شماره ۸، صفحات ۵۱۸-۵۲۲

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